Amyotrophic Lateral Sclerosis Concept

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50bp deletion in the promoter for superoxide dismutase 1 (SOD1) reduces SOD1 expression in vitro and may correlate with increased age of onset of sporadic amyotrophic lateral sclerosis Academic Article
A RANDOMIZED CONTROLLED TRIAL OF RESISTANCE EXERCISE IN INDIVIDUALS WITH ALS Academic Article
A Study of the Purine Derivative AIT-082 in G93A SOD1 Transgenic Mice Academic Article
A comparison of muscle strength testing techniques in amyotrophic lateral sclerosis Academic Article
A genome-wide association study of sporadic ALS in a homogenous Irish population Academic Article
A longitudinal study of the pathophysiological changes in single human thenar motor units in amyotrophic lateral sclerosis Academic Article
A novel candidate region for ALS on chromosome 14q11.2 Academic Article
A randomized controlled trial of resistance exercise in individuals with ALS Academic Article
ALS--decision making under uncertainty: a positive approach. Academic Article
ANG mutations segregate with familial and 'sporadic' amyotrophic lateral sclerosis Academic Article
Amyotrophic Lateral Sclerosis Academic Article
An Unusual Subacute Progressive Motor Neuronopathy with Myasthenia-like Features Academic Article
An electrophysiological estimation of the number of motor units and rate of decay of motor units in amyotrophic lateral sclerosis. Academic Article
Analysis of IFT74as a candidate gene for chromosome 9p-linked ALS-FTD Academic Article
Angiogenin Levels and ANG Genotypes: Dysregulation in Amyotrophic Lateral Sclerosis Academic Article
Assessing Patient Perspectives on Receiving Bad News: A Survey of 1337 Patients With Life-Changing Diagnoses Academic Article
Association of the H63D polymorphism in the hemochromatosis gene with sporadic ALS Academic Article
Author response to a Letter to the Editor entitled: Edaravone administration in pivotal clinical study 19 (Authors: Genge, Angela; Brooks, Benjamin) Academic Article
Beneficial effect of ginseng root in SOD-1 (G93A) transgenic mice Academic Article
C9ORF72 hexanucleotide repeat expansions in patients with ALS from the Coriell Cell Repository Academic Article
Caloric Restriction Shortens Lifespan through an Increase in Lipid Peroxidation, Inflammation and Apoptosis in the G93A Mouse, an Animal Model of ALS Academic Article
Caloric restriction transiently improves motor performance but hastens clinical onset of disease in the Cu/Zn-superoxide dismutase mutant G93A mouse Academic Article
Canadian best practice recommendations for the management of amyotrophic lateral sclerosis Academic Article
Cerebrospinal fluid from patients with amyotrophic lateral sclerosis inhibits sonic hedgehog function Academic Article
Characterization of DCTN1 genetic variability in neurodegeneration Academic Article
Childhood amyotrophic lateral sclerosis caused by excess sphingolipid synthesis Academic Article
Clinicopathological features of primary lateral sclerosis are different from amyotrophic lateral sclerosis Academic Article
Cognitive Deterioration and Functional Compensation in ALS Measured with fMRI Using an Inhibitory Task Academic Article
Control of Motoneuron Survival by Angiogenin Academic Article
Creatine supplementation and riluzole treatment provide similar beneficial effects in copper, zinc superoxide dismutase (G93A) transgenic mice Academic Article
Crosstalk between Notch and Sonic hedgehog signaling in a mouse model of amyotrophic lateral sclerosis Academic Article
Discovery of a Biomarker and Lead Small Molecules to Target r(GGGGCC)-Associated Defects in c9FTD/ALS Academic Article
Effects of age, temperature, and disease on the refractoriness of human nerve and muscle. Academic Article
Effects of high-intensity endurance exercise training in the G93A mouse model of amyotrophic lateral sclerosis Academic Article
Efficacy of minocycline in patients with amyotrophic lateral sclerosis: a phase III randomised trial Academic Article
Elevated serum angiogenin levels in ALS Academic Article
Evaluation of the Golgi trafficking protein VPS54 (wobbler) as a candidate for ALS Academic Article
Familial Amyotrophic Lateral Sclerosis Academic Article
Functional compensation in partially denervated muscles Academic Article
Functional compensation of human motor units in health and disease Academic Article
Genetic testing for amyotrophic lateral sclerosis in Canada – an assessment of current practices Academic Article
Heterozygous frameshift variants in HNRNPA2B1 cause early-onset oculopharyngeal muscular dystrophy Academic Article
Human motor units in health and disease Academic Article
Immunoreactivity of the phosphorylated axonal neurofilament H subunit (pNF-H) in blood of ALS model rodents and ALS patients: evaluation of blood pNF-H as a potential ALS biomarker Academic Article
Impact of Treadmill Running and Sex on Hippocampal Neurogenesis in the Mouse Model of Amyotrophic Lateral Sclerosis Academic Article
Innate immunity in amyotrophic lateral sclerosis Academic Article
Intentions of Canadian health professionals towards recommending exercise for people living with ALS Academic Article
Is edaravone harmful? (A placebo is not a control) Academic Article
Lack of Effect of Methylene Blue in the SOD1 G93A Mouse Model of Amyotrophic Lateral Sclerosis Academic Article
Lasting impact in families after death from ALS Academic Article
MN-166 (ibudilast) in amyotrophic lateral sclerosis in a Phase IIb/III study: COMBAT-ALS study design Academic Article
MOTONEURONE DISEASE AND AGEING Academic Article
Maintaining Quality of Life Academic Article
Manganese Superoxide Dismutase Levels Are Elevated in a Proportion of Amyotrophic Lateral Sclerosis Patient Cell Lines Academic Article
Methods for Estimating the Numbers of Motor Units in Human Muscles Academic Article
Motor unit estimates in the biceps-brachialis in amyotrophic lateral sclerosis Academic Article
Motor unit estimations in small muscles of the hand Academic Article
Motor-evoked responses in primary lateral sclerosis Academic Article
Novel p.Ile151Val mutation in VCP in a patient of African American descent with sporadic ALS Academic Article
One Universal Common Endpoint in Mouse Models of Amyotrophic Lateral Sclerosis Academic Article
PRIMARY LATERAL SCLEROSIS: CLINICAL FEATURES, NEUROPATHOLOGY AND DIAGNOSTIC CRITERIA Academic Article
Paraoxonase promoter and intronic variants modify risk of sporadic amyotrophic lateral sclerosis Academic Article
Pathological laughing and crying in amyotrophic lateral sclerosis: an association with prefrontal cognitive dysfunction Academic Article
Phase II/III randomized trial of TCH346 in patients with ALS Academic Article
Phosphorylated neurofilament heavy subunit (pNF-H) in peripheral blood and CSF as a potential prognostic biomarker in amyotrophic lateral sclerosis Academic Article
Physical Therapy for a Patient Through Six Stages of Amyotrophic Lateral Sclerosis Academic Article
Progranulin mutations and amyotrophic lateral sclerosis or amyotrophic lateral sclerosis-frontotemporal dementia phenotypes Academic Article
Reappraisal of an ALS trial: unaccounted procedural risk Academic Article
Reduced C9orf72 gene expression in c9FTD/ALS is caused by histone trimethylation, an epigenetic event detectable in blood Academic Article
Refining items for a preference-based, amyotrophic lateral sclerosis specific, health-related quality of life scale Academic Article
Reviewing the evidence for viruses as environmental risk factors for ALS: A new perspective Academic Article
SUBCUTANEOUS IGF-1 IS NOT BENEFICIAL IN 2-YEAR ALS TRIAL Academic Article
Safety and efficacy of oral levosimendan in people with amyotrophic lateral sclerosis (the REFALS study): a randomised, double-blind, placebo-controlled phase 3 trial Academic Article
Screening of hypoxia-inducible genes in sporadic ALS Academic Article
Senataxin suppresses the antiviral transcriptional response and controls viral biogenesis Academic Article
Sodium Phenylbutyrate–Taurursodiol for ALS Academic Article
Sonic Hedgehog is Cytoprotective against Oxidative Challenge in a Cellular Model of Amyotrophic Lateral Sclerosis Academic Article
Subcutaneous IGF-1 is not beneficial in 2-year ALS trial Academic Article
TARDBP mutations in individuals with sporadic and familial amyotrophic lateral sclerosis Academic Article
Targeting cellular energy production in neurological disorders. Academic Article
The Effects of Partial Chronic Denervation on Forearm Metabolism Academic Article
The complement factor C5a receptor is upregulated in NFL−/− mouse motor neurons Academic Article
The complex genetics of amyotrophic lateral sclerosis Academic Article
The extent and time course of motoneuron involvement in amyotrophic lateral sclerosis Academic Article
The impact of rehabilitative interventions on quality of life: a qualitative evidence synthesis of personal experiences of individuals with amyotrophic lateral sclerosis Academic Article
Therapeutic exercise for people with amyotrophic lateral sclerosis or motor neuron disease Academic Article
Therapeutic exercise for people with amyotrophic lateral sclerosis or motor neuron disease Academic Article
Transient caloric restriction in early adulthood hastens disease endpoint in male, but not female, Cu/Zn-SOD mutant G93A mice Academic Article
Trophic and proliferative effects of Shh on motor neurons in embryonic spinal cord culture from wildtype and G93A SOD1 mice Academic Article
Variation of Phenotype in Charcot-Marie-Tooth Disease Academic Article
Why is ALS so Difficult to Treat? Academic Article