Journal article
Hydranencephaly complicated by central diabetes insipidus: report of two cases and systematic review of literature
Abstract
PurposeHydranencephaly is a congenital condition characterized by the complete or near-complete absence of the cerebral cortex and basal ganglia, while central diabetes insipidus (CDI) is a condition characterized by the inability to concentrate urine due to a deficiency in antidiuretic hormone (ADH). CDI is known to occur in midline congenital malformations such as holoprosencephaly and septo-optic dysplasia, but its association with …
Authors
Omar AT; Khu KJO
Journal
Child's Nervous System, Vol. 35, No. 7, pp. 1165–1171
Publisher
Springer Nature
Publication Date
July 2019
DOI
10.1007/s00381-019-04137-9
ISSN
0256-7040