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Comparative analysis of Shwachman‐Diamond syndrome...
Journal article

Comparative analysis of Shwachman‐Diamond syndrome to other inherited bone marrow failure syndromes and genotype–phenotype correlation

Abstract

Our knowledge of the phenotypes of inherited bone marrow failure syndromes (IBMFSs) derives from case reports or case series in which only one IBMFS was studied. However, the substantial phenotypic overlap necessitates comparative analysis between the IBMFSs. Shwachman-Diamond syndrome (SDS) is an IBMFS that the appreciation of what comprises its clinical phenotype is still evolving. In this analysis we used data on 125 patients from the …

Authors

Hashmi S; Allen C; Klaassen R; Fernandez C; Yanofsky R; Shereck E; Champagne J; Silva M; Lipton J; Brossard J

Journal

Clinical Genetics, Vol. 79, No. 5, pp. 448–458

Publisher

Wiley

Publication Date

May 2011

DOI

10.1111/j.1399-0004.2010.01468.x

ISSN

0009-9163