The justification for the progressive fibrotic phenotype

PURPOSE OF REVIEW: Describe the concept and recent data for the concept of progressive fibrotic interstitial lung disease (ILD). RECENT FINDINGS: Making an accurate diagnosis is critical to help determine appropriate therapy and predict prognosis. This is certainly true in the field of ILD where a diagnosis of idiopathic pulmonary fibrosis (IPF) leads a clinician to consider initiation of antifibrotic therapy, and avoidance of immunosuppression …