A Case of Sturge–Weber Syndrome with Bilateral Leptomeningeal Involvement

A 40-year-old man with a diagnosis of Sturge–Weber Syndrome (SWS) was admitted to hospital with fever and urosepsis. The sequelae of this condition include seizures, intellectual disability, bilateral glaucoma, hypothyroidism, and diffuse port-wine stain. He was also noted to have several pyogenic granulomas and a large capillary malformation of the lower lip, with associated bleeding risk. Clinical images highlight the diagnostic cues and dermatologic manifestations that are associated with SWS. Management of patients with this condition requires multidisciplinary care of the neurologic, endocrine, and vascular complications of SWS, in addition to extensive psychosocial support.