The Congenital Intrahepatic Arterioportal Fistula Syndrome Journal Articles

abstract

• ABSTRACTCongenital intrahepatic arterioportal fistula is a rare but treatable cause of portal hypertension for which early recognition may lead to successful radiological management. We report an infant presenting with severe failure to thrive, melena and splenomegaly due to a congenital intrahepatic arterioportal fistula, successfully ablated after multiple trials of superselective transarterial embolization. Comprehensive review of congenital cases provides an understanding of the key clinical features defining this syndrome. A classification system is proposed, upon which treatment decisions may be based.

authors

• Norton, Seamus
• Jacobson, Kevan
• Moroz, Stanley P
• Culham, Gordon
• Ng, Vicky
• Turner, Justine
• John, Philip

status

• published 

publication date

• August 2006

has subject area

• 11 Medical and Health Sciences (FoR)
• Abdominal Pain (MeSH)
• Arteriovenous Fistula (MeSH)
• Child, Preschool (MeSH)
• Embolization, Therapeutic (MeSH)
• Failure to Thrive (MeSH)
• Gastroenterology & Hepatology (Science Metrix)
• Hepatic Artery (MeSH)
• Humans (MeSH)
• Hypertension, Portal (MeSH)
• Infant (MeSH)
• Male (MeSH)
• Portal Vein (MeSH)
• Tomography, X-Ray Computed (MeSH)
• Treatment Outcome (MeSH)

published in

• Journal of Pediatric Gastroenterology and Nutrition  Journal

keywords

• Abdominal Pain
• Arteriovenous Fistula
• Child, Preschool
• Embolization, Therapeutic
• Failure to Thrive
• Hepatic Artery
• Humans
• Hypertension, Portal
• Infant
• Male
• Portal Vein
• Tomography, X-Ray Computed
• Treatment Outcome

Digital Object Identifier (DOI)

• 10.1097/01.mpg.0000221890.13630.ad

PubMed ID

• 16877994

start page

• 248

end page

• 255

volume

• 43

issue

• 2