Malignant Rhabdoid Tumour of the Pineal Region Academic Article uri icon

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abstract

  • Abstract:A 9-month-old male presented to hospital with signs and symptoms of raised intracranial pressure. A CT scan showed obstructive hydrocephalus from a large pineal region mass lesion into which an intratumoral hemorrhage had occurred. A posterior fossa craniectomy and subtotal excision of the mass lesion were performed. By histopathology, the lesion was a malignant rhabdoid tumour (MRT). Despite surgery and chemotherapy, the tumour grew inexorably, and the patient died four months after the initial diagnosis. MRT is a rare and highly invasive neoplasm which infrequently arises from the central nervous system. This is the first documented case of a MRT arising from the pineal region. The clinical, radiographic, and pathological features of the MRT in this patient are presented.

authors

  • Muller, Matthew
  • Hubbard, Sherri Lynn
  • Provias, John
  • Greenberg, Mark
  • Becker, Laurence E
  • Rutka, James T

publication date

  • August 1994