Update in the diagnostic approach to fibrotic interstitial lung disease

Fibrotic interstitial lung disease (ILD) is increasingly recognized as an important cause of chronic pulmonary disease. Although ILDs can be challenging to diagnose and manage, there have been a number of recent developments aimed at improving the accuracy of establishing a confident underlying diagnosis. This Clinical Respiratory Review summarizes recent developments in the diagnostic approach to some of the most common forms of fibrotic ILD, including idiopathic pulmonary fibrosis, chronic hypersensitivity pneumonitis, idiopathic nonspecific interstitial pneumonia, and unclassifiable ILD. In this review, we have summarized international consensus guidelines, working group reports, and other clinically relevant and highly impactful publications.