Journal article
Sickle cell disease in Saudi Arabia: the phenotype in adults with the Arab‐Indian haplotype is not benign
Abstract
Sickle cell disease (SCD) in Saudi patients from the Eastern Province is associated with the Arab-Indian (AI) HBB (β-globin gene) haplotype. The phenotype of AI SCD in children was described as benign and was attributed to their high fetal haemoglobin (HbF). We conducted a hospital-based study to assess the pattern of SCD complications in adults. A total of 104 patients with average age of 27 years were enrolled. Ninety-six per cent of these …
Authors
Alsultan A; Alabdulaali MK; Griffin PJ; AlSuliman AM; Ghabbour HA; Sebastiani P; Albuali WH; Al‐Ali AK; Chui DHK; Steinberg MH
Journal
British Journal of Haematology, Vol. 164, No. 4, pp. 597–604
Publisher
Wiley
Publication Date
February 2014
DOI
10.1111/bjh.12650
ISSN
0007-1048